GBE1 (NM_000158) Human Untagged Clone

CAT#: SC120081

GBE1 (untagged)-Human glucan (1,4-alpha-), branching enzyme 1 (GBE1)



  "NM_000158" in other vectors (5)

CNY 2,950.00


货期*
现货

规格
    • 10 ug

Product images

经常一起买 (4)
GBE1 mouse monoclonal antibody, clone OTI1D11 (formerly 1D11)
    • 100 ul

CNY 1,999.00
CNY 2,700.00


TurboFectin Transfection Reagent (1 mL in 1 vial)
    • 1 ml in 1 vial

CNY 4,090.00


DH5α Chemically Competent Cells (≥10^8 cfu/μg of pUC19 DNA)
    • 5 x 200 ul

CNY 1,280.00


Forward sequencing primer VP1.5, Reverse sequencing primer XL39, 100pmoles each
    • 100 pmol

CNY 480.00

Specifications

Product Data
Type Human Untagged Clone
Tag Tag Free
Synonyms APBD; GBE; GSD4
Vector pCMV6-XL5
E. coli Selection Ampicillin (100 ug/mL)
Mammalian Cell Selection None
Sequence Data
>OriGene ORF within SC120081 sequence for NM_000158 edited (data generated by NextGen Sequencing)
ATGGCGGCTCCGATGACTCCCGCGGCTCGGCCCGAGGACTACGAGGCGGCGCTCAATGCC
GCCCTGGCTGACGTGCCCGAACTGGCCAGACTCCTGGAGATCGACCCGTACTTGAAGCCC
TACGCCGTGGACTTCCAGCGCAGGTATAAGCAGTTTAGCCAAATTTTGAAGAACATTGGA
GAAAATGAAGGTGGTATTGATAAGTTTTCCAGAGGCTATGAATCATTTGGCGTCCACAGA
TGTGCTGATGGTGGTTTATACTGCAAAGAATGGGCCCCGGGAGCAGAAGGAGTTTTTCTT
ACTGGAGATTTTAATGGTTGGAATCCATTTTCGTACCCATACAAAAAACTGGATTATGGA
AAATGGGAGCTGTATATCCCACCAAAGCAGAATAAATCTGTACTCGTGCCTCATGGATCC
AAATTAAAGGTAGTTATTACTAGTAAAAGCGGAGAGATCTTGTATCGTATTTCACCGTGG
GCAAAGTATGTGGTTCGTGAAGGTGATAATGTGAATTATGATTGGATACACTGGGATCCA
GAACACTCATATGAGTTTAAGCATTCCAGACCAAAGAAGCCACGGAGTCTAAGAATTTAT
GAATCTCATGTGGGAATTTCTTCCCATGAAGGAAAAGTAGCTTCTTATAAACATTTTACA
TGCAATGTACTACCAAGAATCAAAGGCCTTGGATACAACTGCATTCAGTTGATGGCAATC
ATGGAGCATGCTTACTATGCCAGCTTTGGTTACCAAATCACAAGCTTCTTTGCAGCTTCC
AGCCGTTATGGAACACCTGAAGAGCTACAAGAACTGGTAGACACAGCTCATTCCATGGGT
ATCATAGTCCTCTTAGATGTGGTACACAGCCATGCTTCAAAAAATTCAGCAGATGGATTG
AATATGTTTGATGGGACAGATTCCTGTTATTTTCATTCTGGACCTAGAGGGACTCATGAT
CTTTGGGATAGCAGATTGTTTGCCTACTCCAGCTGGGAAGTTTTAAGATTCCTTCTGTCA
AACATAAGATGGTGGTTGGAAGAATATCGCTTTGATGGATTTCGTTTTGATGGTGTTACG
TCCATGCTTTATCATCACCATGGAGTGGGTCAAGGTTTCTCAGGTGATTACAGTGAATAT
TTCGGACTACAAGTAGATGAAGATGCCTTGACTTACCTCATGTTGGCAAATCATTTGGTT
CACACGCTGTGTCCCGATTCTATAACAATAGCTGAGGATGTATCAGGAATGCCAGCTCTG
TGCTCTCCAATTTCCCAGGGAGGGGGTGGTTTTGACTATCGACTAGCCATGGCAATTCCA
GATAAGTGGATTCAGCTACTTAAAGAGTTTAAAGATGAAGACTGGAACATGGGCGATATA
GTATACACGCTCACAAACAGGCGCTACCTTGAAAAGTGCATTGCTTATGCAGAGAGCCAT
GATCAGGCATTGGTTGGGGATAAGTCGCTGGCATTTTGGTTGATGGATGCCGAAATGTAT
ACAAACATGAGTGTCCTGACTCCTTTTACTCCAGTTATTGATCGTGGAATACAGCTTCAT
AAAATGATTCGACTCATTACGCATGGGCTTGGTGGAGAAGGCTATCTCAATTTCATGGGT
AATGAATTTGGGCATCCTGAATGGTTAGACTTCCCAAGAAAAGGAAATAATGAGAGTTAC
CATTATGCCAGGCGGCAGTTTCATTTAACTGACGACGACCTTCTTCGCTACAAGTTCCTA
AATAATTTTGACAGGGATATGAATAGATTGGAAGAAAGATATGGTTGGCTTGCAGCTCCA
CAGGCCTACGTGAGTGAAAAACATGAAGGCAATAAGATCATTGCTTTTGAAAGAGCAGGT
CTTCTTTTCATTTTCAACTTCCATCCAAGCAAGAGCTACACTGACTACCGAGTTGGAACA
GCATTGCCAGGGAAATTCAAAATTGTGCTAGATTCAGATGCAGCGGAATATGGAGGGCAT
CAGAGACTGGACCACAGCACTGACTTTTTTTCTGAGGCTTTTGAACATAATGGGCGTCCC
TATTCTCTTTTGGTGTACATTCCAAGCAGAGTGGCCCTCATCCTTCAGAATGTGGATCTG
CCGAATTGA

Clone variation with respect to NM_000158.3
>OriGene 5' read for NM_000158 unedited
GGATACGACTCACTATAGGGCGGCCGCGAATTCGGCACGAGGCACGCCTAGGCGCCCTCC
GGCTCCGCCCTAGCCGCCGCGTCCCAGCTAGAGCTCCAGCGCCCGCTCAGGCCCCACTCG
ACCCTCTCGGGCCTCGGCTACTTGGACTGCGGCGGAATATGGCGGCTCCGATGACTCCCG
CGGCTCGGCCCGAGGACTACGAGGCGGCGCTCAATGCCGCCCTGGCTGACGTGCCCGAAC
TGGCCAGACTCCTGGAGATCGACCCGTACTTGAAGCCCTACGCCGTGGACTTCCAGCGCA
GGTATAAGCAGTTTAGCCAAATTTTGAAGAACATTGGAGAAAATGAAGGTGGTATTGATA
AGTTTTCCAGAGGCTATGAATCATTTGGCGTCCACAGATGTGCTGATGGTGGTTTATACT
GCAAAGAATGGGCCCCGGGAGCAGAAGGAGTTTTTCTTACTGGAGATTTTAATGGTTGGA
ATCCATTTTCGTACCCATACAAAAAACTGGATTATGGAAAATGGGAGCTGTATATCCCAC
CAAAGCAGAATAAATCTGTACTCGTGCCTCATGGATCCAAATTAAAGGTAGTTATTACTA
GTAAAAGCGGAGAGATCTTGTATCGTATTTCACCGTGGGCAAAGTATGTGGTTCGTGAAG
GGTGATATGTGAATTATGATTGGATACACTGGGATCCAGAACACTCATATGAGNTTAAGC
ATTCCAGACCAAAGAAGCCACGGAGTCTAAGAAATTATGAATCTCATGTGGGGAATTTCT
TCCCATGGAAGGAAAGTAGCTTCCTTATAACCATTTTACATGCCATGGTACTANCCANGA
ATCANAGGCCCTGGNATACCAACTGCATCAGNTGGATGGCANTCATGGGAGCATGCTTAC
TATGCCAGNCTTTGGNTACCAAATCACAAGCTTCTTTGCAGCCTCCAGCCCGTTATGC
>OriGene 3' read for NM_000158 unedited
CCGCGGCCGCAATCTAGAGTCGAGTTTTTTTTTTTTTTTTTTTTTTTTTTTTTTTTTACA
AAAGCTTTTTATTGATTGAAATGAAAGACATTTTCTGAAATGCTACAATTACCATTTCAG
GGCTTCAGAAAGACTGAGATACTGGCATTTAACAAGATACTTAGTGGACAAGAGATCACA
AAATAAAACACAAAATGAGACACGGATGAGTTCATACGTAATGGCTTTTATATTACCTTG
GATATAATTCTTTATATCACTACTGCATATTTATTACAGTATTTCTAAACACAATTTGAA
AAAAAGAAACAAAGAAACAATCTTGGTACCTCATAATTTAGACCAAAAGATATCAGAACA
AATAGAGCCACCAAATATCCATCTTAAATACTGGGTACATTTAACAGAAATAATCATACA
TGACAAATGATTCAAATTTGAATTTAAAAGGATCAAATAATTAGCCAGGAAAGCAAAATG
TTTTTAACATATTATATATAACACTTCCATTTGAGAATCCTAGCTGCTAAGATGACTTGA
AAATATGGTCTAGGATTCCTAATATTTTAAACATATTCTCCTATCTACTTAAATAAAAGT
TTGCTGTATTTGCATAAACCAATATTGAATTTCAGACACTTGATGGCTTGGCTAGACAAC
TGTATTCTGAAAAGCATACATGTTATAAGCTGTGTGANCAGTGATACCAGAAAACAAAAC
ACANATCTGCATCTGGTGGAGCTGAAATCAGGCCTCTTCAATTCGGCAGATCCACATTCT
GAAGGATGAGGGCCACTCTGCTTGGNAGTACACCANAAGAGAATAGGNNACGCCATTATG
TTCAAAAGCCTCAGAAAAAAATCAGTGCTGTGGTACAGTCTCTGATGCCCTNCATATCCG
CTGCATCTGAATCTAGCACATTTTGAATTNCCTGGCA
Restriction Sites NotI-NotI     
ACCN NM_000158
Insert Size 3160 bp
OTI Disclaimer Our molecular clone sequence data has been matched to the reference identifier above as a point of reference. Note that the complete sequence of our molecular clones may differ from the sequence published for this corresponding reference, e.g., by representing an alternative RNA splicing form or single nucleotide polymorphism (SNP).
Product Components The ORF clone is ion-exchange column purified and shipped in a 2D barcoded Matrix tube containing 10ug of transfection-ready, dried plasmid DNA (reconstitute with 100 ul of water).
Reconstitution 1. Centrifuge at 5,000xg for 5min.
2. Carefully open the tube and add 100ul of sterile water to dissolve the DNA.
3. Close the tube and incubate for 10 minutes at room temperature.
4. Briefly vortex the tube and then do a quick spin (less than 5000xg) to concentrate the liquid at the bottom.
5. Store the suspended plasmid at -20°C. The DNA is stable for at least one year from date of shipping when stored at -20°C.
Reference Data
RefSeq NM_000158.1, NP_000149.1
RefSeq Size 2913 bp
RefSeq ORF 2109 bp
Locus ID 2632
UniProt ID Q04446
Domains isoamylase_N, alpha-amylase, Aamy
Protein Families Druggable Genome
Protein Pathways Metabolic pathways, Starch and sucrose metabolism
Gene Summary The protein encoded by this gene is a glycogen branching enzyme that catalyzes the transfer of alpha-1,4-linked glucosyl units from the outer end of a glycogen chain to an alpha-1,6 position on the same or a neighboring glycogen chain. Branching of the chains is essential to increase the solubility of the glycogen molecule and, consequently, in reducing the osmotic pressure within cells. Highest level of this enzyme are found in liver and muscle. Mutations in this gene are associated with glycogen storage disease IV (also known as Andersen's disease). [provided by RefSeq, Jul 2008]
*Delivery time may vary from web posted schedule. Occasional delays may occur due to unforeseen complexities in the preparation of your product. International customers may expect an additional 1-2 weeks in shipping.

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