Nebulin (NEB) Mouse Monoclonal Antibody [Clone ID: Neb-20]

Specifications

Product Data
Clone Name	Neb-20
Applications	WB
Recommend Dilution	Western Blot: 1 - 2 μg/ml.
Reactivity	Chicken, Frog, Human, Mouse, Rat
Host	Mouse
Clonality	Monoclonal
Immunogen	Chicken breast nebulin
Specificity	This antibody reacts to Nebulin.
Isotype	IgG1
Formulation	1.2 % sodium acetate, with 2 mg BSA and 0.01 mg sodium azide as preservative State: Purified State: Lyphilized purified Ig fraction
Reconstitution Method	Restore with 1.2% sodium acetate or neutral PBS
Concentration	0,1 mg/ml (after reconstitution with PBS)
Purification	Affinity chromatography
Conjugation	Unconjugated
Storage Condition	Prior to reconstitution store at -20°C. Following reconstitution store undiluted at 2-8°C for one month or (in aliquots) at -20°C for longer. Avoid repeated freezing and thawing.
Gene Name	nebulin
Database Link	Entrez Gene 4703 Human UniProt ID P20929
Background	Nebulin is a giant protein component of the cytoskeletal matrix that coexists with the thick and thin filaments within the sarcomeres of skeletal muscle. In most vertebrates, nebulin accounts for 3 to 4% of the total myofibrillar protein and its size varies from 600 to 800 kD in a manner that is tissue-, species-,and developmental stage-specific. The nebulin gene contains 183 exons in a 249-kb genomic region. Nebulin is mapped to chromosome 2. Nebulin is a giant filamentous protein specific for vertebrate skeletal muscles. Mutations in the nebulin gene associated with autosomal recessive nemaline myopathy.
Synonyms	NEB
Reference Data

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