Strumpellin (WASHC5) (NM_014846) Human Untagged Clone

CAT#: SC127327

KIAA0196 (untagged)-Human KIAA0196 (KIAA0196)



  "NM_014846" in other vectors (4)

CNY 8080.00


货期*
现货

规格
    • 10 ug

Product images

推荐一起购买 (4)
KIAA0196 Rabbit polyclonal Antibody
    • 100 ul

CNY 1999.00
CNY 3280.00


TurboFectin Transfection Reagent (1 mL in 1 vial)
    • 1 ml in 1 vial

CNY 4090.00


DH5α Chemically Competent Cells (≥10^8 cfu/μg of pUC19 DNA)
    • 5 x 200 ul

CNY 1280.00


Forward sequencing primer VP1.5, Reverse sequencing primer XL39, 100pmoles each
    • 100 pmol

CNY 480.00

Specifications

Product Data
Type Human Untagged Clone
Tag Tag Free
Synonyms KIAA0196; RTSC; RTSC1; SPG8
Vector pCMV6-XL4
E. coli Selection Ampicillin (100 ug/mL)
Mammalian Cell Selection None
Sequence Data
>OriGene ORF within SC127327 sequence for NM_014846 edited (data generated by NextGen Sequencing)
ATGTTGGACTTTCTAGCCGAGAACAACCTCTGTGGCCAAGCAATCCTAAGGATTGTTTCC
TGTGGTAATGCCATCATTGCTGAACTTTTGAGACTCTCTGAGTTTATTCCTGCTGTGTTC
AGGTTAAAAGACAGAGCTGATCAACAGAAATATGGAGATATCATATTTGATTTCAGCTAT
TTTAAGGGTCCAGAATTATGGGAAAGCAAACTGGATGCTAAGCCAGAGCTACAGGATTTA
GATGAAGAATTTCGTGAAAACAACATAGAAATTGTGACCAGATTTTATTTAGCATTTCAA
AGTGTACATAAATATATTGTAGACTTAAACAGATATCTAGATGATCTCAATGAAGGGGTT
TATATTCAGCAAACCTTAGAAACTGTGCTTCTCAATGAAGATGGAAAACAACTTCTATGT
GAAGCACTGTACTTATATGGAGTTATGCTACTGGTCATTGACCAAAAGATTGAAGGAGAA
GTCAGAGAGAGGATGCTGGTTTCTTACTACCGATACAGTGCTGCTCGATCTTCTGCTGAT
TCAAATATGGACGATATTTGTAAGCTGCTTCGAAGTACAGGTTATTCTAGCCAACCAGGT
GCCAAAAGACCATCCAACTATCCCGAGAGCTATTTCCAGAGAGTGCCTATCAACGAATCC
TTCATCAGTATGGTCATTGGTCGACTGAGATCTGATGATATTTACAACCAGGTCTCAGCG
TATCCTTTGCCGGAGCATCGCAGCACAGCCCTGGCAAACCAAGCTGCCATGCTGTACGTG
ATTCTCTACTTTGAGCCTTCCATCCTTCACACCCATCAAGCAAAAATGAGAGAGATAGTG
GATAAATACTTTCCAGATAATTGGGTAATTAGTATTTACATGGGGATCACAGTTAATCTA
GTAGATGCTTGGGAACCTTACAAAGCTGCAAAAACTGCTTTAAATAATACCCTGGACCTT
TCAAATGTCAGAGAACAGGCAAGCAGATATGCTACTGTCAGTGAAAGAGTGCATGCTCAA
GTGCAGCAATTTCTAAAAGAAGGTTATTTAAGGGAGGAGATGGTTCTGGACAATATCCCA
AAGCTTCTGAACTGCCTGAGAGACTGCAATGTTGCCATCCGATGGCTGATGCTTCATACA
GCAGACTCAGCCTGTGACCCAAACAACAAACGCCTTCGTCAAATCAAGGACCAGATTCTA
ACAGACTCTCGGTACAATCCCAGGATCCTCTTCCAGCTGCTGTTAGATACTGCACAATTT
GAGTTTATACTCAAAGAGATGTTCAAGCAAATGCTTTCAGAAAAGCAAACCAAATGGGAG
CATTACAAGAAAGAGGGTTCGGAGCGGATGACTGAGCTTGCTGATGTCTTTTCAGGAGTG
AAACCCCTAACCAGAGTGGAGAAAAATGAAAACCTTCAAGCTTGGTTCAGAGAGATCTCA
AAACAAATATTGTCTTTAAATTATGATGATTCTACTGCTGCGGGCAGAAAAACTGTACAA
CTGATACAAGCTTTGGAAGAGGTTCAAGAATTCCACCAGTTGGAATCCAATCTGCAAGTA
TGTCAGTTTCTTGCCGATACTCGAAAGTTTCTTCATCAAATGATCAGAACCATTAACATT
AAAGAGGAGGTTCTGATCACAATGCAGATCGTTGGGGACCTTTCTTTCGCTTGGCAGTTG
ATTGACAGTTTCACATCCATCATGCAAGAAAGCATAAGGGTAAATCCATCCATGGTTACT
AAACTCAGAGCTACCTTCCTAAAGCTTGCCTCTGCCCTCGATCTGCCCCTTCTTCGTATT
AATCAGGCAAATAGCCCCGACCTGCTCAGCGTGTCACAGTACTATTCTGGAGAGTTGGTA
TCCTATGTGAGAAAAGTTTTGCAGATCATCCCAGAAAGCATGTTTACATCTCTTCTAAAG
ATCATAAAGCTTCAGACCCACGACATTATTGAAGTGCCTACCCGCCTGGACAAAGACAAG
CTGAGGGACTATGCTCAGCTAGGCCCACGATACGAGGTTGCCAAGCTTACTCATGCTATT
TCCATTTTTACTGAAGGCATCTTAATGATGAAAACGACTTTGGTTGGCATCATCAAGGTG
GATCCAAAGCAGTTGCTGGAAGATGGAATAAGGAAAGAGCTTGTGAAGCGCGTTGCCTTT
GCCCTGCATAGGGGACTGATATTCAACCCTCGAGCCAAGCCAAGTGAATTGATGCCCAAG
CTGAAAGAGTTGGGAGCGACCATGGATGGATTCCATCGTTCTTTTGAATACATACAGGAC
TATGTCAACATTTATGGTCTGAAGATTTGGCAGGAAGAAGTATCTCGTATCATAAATTAC
AACGTGGAGCAAGAGTGTAATAACTTTCTAAGAACGAAGATTCAAGATTGGCAAAGCATG
TACCAGTCCACTCATATTCCAATACCCAAGTTTACCCCTGTGGATGAGTCTGTAACGTTT
ATTGGTCGACTCTGCAGAGAAATCCTGCGGATCACAGACCCAAAAATGACATGTCACATA
GACCAGCTGAACACTTGGTATGATATGAAAACTCATCAGGAAGTGACCAGCAGCCGCCTC
TTCTCAGAAATCCAGACCACCTTGGGAACCTTTGGTCTAAATGGCTTAGACAGGCTTCTG
TGCTTTATGATTGTAAAAGAGTTACAGAATTTCCTCAGTATGTTTCAGAAAATTATCCTG
AGAGACAGAACTGTTCAGGACACTTTAAAAACCCTCATGAATGCTGTCAGTCCCCTAAAA
AGTATTGTCGCAAATTCAAATAAAATTTATTTTTCCGCCATTGCCAAAACACAGAAGATT
TGGACTGCGTATCTCGAGGCTATAATGAAGGTTGGGCAGATGCAGATTCTGAGACAACAG
ATTGCCAATGAATTAAATTATTCTTGTCGGTTTGATTCTAAACATCTGGCAGCTGCTCTG
GAGAATCTCAATAAGGCTCTCCTAGCAGACATTGAAGCCCACTATCAGGACCCTTCACTT
CCTTACCCCAAAGAAGATAACACACTTTTATATGAAATCACAGCCTATCTGGAGGCAGCT
GGCATTCACAACCCACTGAATAAGATATACATAACAACAAAGCGCTTACCCTATTTTCCA
ATTGTAAACTTTCTATTTTTGATCGCTCAGTTGCCAAAACTTCAATACAACAAAAATCTG
GGAATGGTCTGCCGAAAACCGACCGACCCGGTTGATTGGCCACCACTTGTCCTGGGACTG
CTCACTCTGCTGAAGCAGTTCCATTCCCGGTACACCGAGCAGTTCCTGGCGCTGATTGGC
CAGTTTATCTGCTCCACGGTGGAGCAGTGTACAAGCCAGAAGATACCTGAAATTCCTGCA
GATGTTGTGGGTGCCCTTCTGTTCCTGGAGGATTATGTTCGGTACACAAAGCTACCCAGG
AGGGTTGCTGAAGCACATGTGCCTAATTTCATTTTTGATGAGTTCAGAACAGTGCTGTAA

Clone variation with respect to NM_014846.3
>OriGene 5' read for NM_014846 unedited
CGGCCGCGAATTCGGCACGAGGTCGGGGTCTGACCCGCTCCAGGTCCGGGACTGCGGATA
GAAGAGGACCGCCGCCTTGAGGGAGGGGTGGAAACTGGGTGCCGGCTCCGCGCGCGACCT
CCGGCCCTGCGCGTGCGCCGTGGCGCGGCCCGGCTGACAGGTTCTTTAATGGAGGAGCCA
ATCTCTCTGCACACCTGGTTTCATCTAATAATATACAGACACCAGCTCTGAGGCCAGTTA
ATCATCCCCAGTGTCCAGGCACAGAGTAGTCGGTCCGCCTCACAATGTTGGACTTTCTAG
CCGAGAACAACCTCTGTGGCCAAGCAATCCTAAGGATTGTTTCCTGTGGTAATGCCATCA
TTGCTGAACTTTTGAGACTCTCTGAGTTTATTCCTGCTGTGTTCAGGTTAAAAGACAGAG
CTGATCAACAGAAATATGGAGATATCATATTTGATTTCAGCTATTTTAAGGGTCCAGAAT
TATGGGAAAGCAAACTGGATGCTAAGCCAGAGCTACAGGATTTAGATGAAGAATTTCGTG
AAAACAACATAGAAATTGTGACCAGATTTTATTTAGCATTTCAAAGTGTACATAAATATA
TTGTAGACTTAAACAGATATCTAGATGATCTCAATGAAGGGGTTTATATTCAGCANACCT
AGAAACTGTGCTTCTCAATGAGAATGGGAAACACTTCTATGTGAAGCACTGTACTTATAT
GGAGTTA
>OriGene 3' read for NM_014846 unedited
AGTCTTGNACCGCGGCACGCAATCTAGTGTCGAGTTTTTTTTTTTTTTTTTTTTTTTTTT
TTTACTAGTAATACTATTTTACTGAAAATCTGGAGTTGCACAAATAGTTCTTTAAAACAT
AAAACTAAATGGATTTATACATAACAGTTACATTCAGCATTTAAAAAAGGCAGTACAAAA
ATGTGTTCTGCTTTTATCTGATATAAATTGCATGTAATACCATGATTTAAACAATATCAG
TTATATTAACTAATGCCATGAGATATATCTTACTCAAAACGTCTGATGTTTCCCATAATA
GACAGAAACAATGCAGTTGTATGAGCAACTGAGTTTCTTTTCATCTTCAAATTCATTTGT
GATGGGGGGAAAATCTAAGGACAATCCTTCCATTGAAAAAGTAGGAAAAACAGTTACAGC
ACTGTTCTGAACTCATCAAAAATGAAACTAGGCACATGTGCTTCAGCAACCCTCCTGGGT
AGCTTTGTGTACCGAACATAATCCTCCAGGAACAGAAGGGCACCCACAACATCTGCAGGA
ATTTCAGGTATCTTCTGGCTTGTACACTGCTCCACCGTCGAGCAGATAAACTGGCCAATC
AGCGCCAGGAACTGCTCGGTGTACCGGGAATGGCTACTGCTTCACCAGAGTGAGCAGTCC
CAGGACAAGTGGTGGCCAATCACCCGGGTCGGTCGGTTTTTGGCAGACCATTCCCAGATT
TTTGTTGCATTGAAGTTTTGGCCCCTGACCCATCAAAAATAGAAAGTCTACCCCCTGGAA
AATAGGGTAACCCGCCCCGCGGCTATGTATATCTTATTAAAGGGGTCTGTGAATGCCAAC
TTGCCCTCCAAATAATCCTGGGATTCCATATTAAAAGCGTGGTTATTCTTCTCTGGCGGT
AAAGCATAGAAAGGGCCCTGATANTGCGCTCCACAGTCCGCCTAAGAGAACCTATCAGAA
ATCTCCACACCACCTGCCTAGTTTTTATCCAACCCACAGAAAN
Restriction Sites NotI-NotI     
ACCN NM_014846
Insert Size 4090 bp
OTI Disclaimer Our molecular clone sequence data has been matched to the reference identifier above as a point of reference. Note that the complete sequence of our molecular clones may differ from the sequence published for this corresponding reference, e.g., by representing an alternative RNA splicing form or single nucleotide polymorphism (SNP).
Product Components The ORF clone is ion-exchange column purified and shipped in a 2D barcoded Matrix tube containing 10ug of transfection-ready, dried plasmid DNA (reconstitute with 100 ul of water).
Reconstitution 1. Centrifuge at 5,000xg for 5min.
2. Carefully open the tube and add 100ul of sterile water to dissolve the DNA.
3. Close the tube and incubate for 10 minutes at room temperature.
4. Briefly vortex the tube and then do a quick spin (less than 5000xg) to concentrate the liquid at the bottom.
5. Store the suspended plasmid at -20°C. The DNA is stable for at least one year from date of shipping when stored at -20°C.
Note Plasmids are not sterile.  For experiments where strict sterility is required, filtration with 0.22um filter is required.
Reference Data
RefSeq NM_014846.2, NP_055661.2
RefSeq Size 3925 bp
RefSeq ORF 3480 bp
Locus ID 9897
UniProt ID Q12768
Gene Summary This gene encodes a 134 kDa protein named strumpellin that is predicted to have multiple transmembrane domains and a spectrin-repeat-containing domain. This ubiquitously expressed gene has its highest expression in skeletal muscle. The protein is named for Strumpell disease; a form of hereditary spastic paraplegia (HSP). Spastic paraplegias are a diverse group of disorders in which the autosomal dominant forms are characterized by progressive, lower extremity spasticity caused by axonal degeneration in the terminal portions of the longest descending and ascending corticospinal tracts. More than 30 loci (SPG1-33) have been implicated in hereditary spastic paraplegia diseases. [provided by RefSeq, Aug 2009]
*Delivery time may vary from web posted schedule. Occasional delays may occur due to unforeseen complexities in the preparation of your product. International customers may expect an additional 1-2 weeks in shipping.

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